“Pediatric Torticollis” From EM Quick Hits 66

Today, I review, link to, and excerpt from Pediatric Torticollis from Emergency Medicine CasesQuick Hits 66.*

*Helman, A. Schonfeld, D. Swaminathan, A. Petrosoniak, A. Morgenstern, J. Tagg, A. Myers, V. Tintinalli, J. EM Quick Hits 66 – Pediatric Torticollis, Stable Stable Wide Complex Tachydysrhythmias, Post-intubation Neurocritical Care, Hyponatremia Correction Rates, Paronychia Management, Women in EM Leader Series with Judith Tintinalli  https://emergencymedicinecases.com/em-quick-hits-july-2025/Accessed August 9, 2025.

All that follows is from the above resource.

Deborah Schonfeld on pediatric torticollis (02:33 – 28:21)

Play Podcast

Pediatric torticollis: Not just muscular injury

Broad Categories in the differential diagnosis of pediatric torticollis

  • Muscular (SCM/trapezius): Most common; typically resolves within a week.

  • Atlantoaxial Subluxation: C1/2 instability due to ligamentous or osseous abnormalities.

  • Infectious:

    • Viral URTI/Pharyngitis → Referred pain, muscle spasm
    • Retropharyngeal Abscess (typically ages 2–4): Limited neck extension, fever, dysphagia, drooling, stridor
    • Osteomyelitis/Discitis: Cervical spine tenderness
    • Lemierre Syndrome: IJ thrombophlebitis post-oropharyngeal infection → SCM or jugular tenderness/swelling
  • CNS Lesion (typically painless):

    • Up to 20% of posterior fossa tumors present with torticollis
    • 50% of pediatric malignant brain tumors are located in the posterior fossa
    • Clinical red flags: headache, vomiting, gait changes, ataxia, focal neuro deficits

Atlantoaxial Subluxation

Risk Factors for Atlantoaxial Subluxation

  • Ligamentous injury (more common than fracture in children)
  • Congenital hypermobility: Trisomy 21/Down syndrome, Marfan’s Syndrome, Juvenile Idiopathic Arthritis
  • Grisel Syndrome: Post head/neck surgery with local inflammation → ligament laxity

Physical exam pearl to distinguish atlatoaxial subluxation from muscular torticollis

  • Muscular torticollis: Head tilts toward spastic SCM
  • Subluxation: Tilts away from affected side

Imaging for suspected atlantoaxial subluxation

  • XR: Odontoid and lateral views; assess Atlantodental Interval (≤5 mm if <8 years) – use as screening in low pretest probability patients; be aware than sensitivity is poor

    • CT: Gold standard when high suspicion or red flags present

    Bottom Line

    • Most cases of torticollis self-limiting, due to SCM muscle spasm
    • Torticollis >1 week or with neurological findings → Image to rule out subluxation, infection, or CNS lesion

atlantodental interval

Source: Radiopaedia under the Creative Commons Attribution-Noncommercial-Share Alike 3.0 Unported licence

Reference

  1. McInerny, Thomas K, and American Academy of Pediatrics. American Academy of Pediatrics Textbook of Pediatric Care. Washington, D.C: American Academy of Pediatrics, 2009. Print.
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